Paroxysmal Nocturnal Hemoglobinuria: Rare But Real
Paroxysmal Nocturnal Hemoglobinuria (PNH) is a rare disorder with progressive morbidities and mortalities. It is a life threatening disease that causes thrombosis, end organ damage, and impaired quality of life and demands early diagnosis and intervention. The International Clinical Cytometry Society (ICCS) Guidelines and International PNH Interest Group (IPIG) recommend evaluation of high risk patients. Identifying and screening of high risk patients is essential for the diagnosis, management and monitoring of PNH.
